Brief Reports| Volume 54, ISSUE 5, P660-661, November 2001

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Klippel-Trenaunay-Weber syndrome: Role of EUS

      Klippel-Trenaunay-Weber syndrome (KTWS) is a rare syndrome characterized by the triad of a port-wine stain of an extremity, varicose veins, and bony, soft-tissue hypertrophy of the affected limb.
      • Klippel M
      • Trenaunay P.
      Du naevus variqueux osteohypertrophique.
      The GI tract may also be involved, and patients may present with symptoms of bleeding, pain, and diarrhea.
      • Weber FP.
      Angioma formation in connection with hypertrophy of limbs and hemihypertrophy.
      This is a report of a patient with KTWS and an atypical presentation in whom duplex EUS was helpful in establishing the diagnosis.
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